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GeneQ17832889· pop 5· linked from 34 articles

Also known as ATX1, HAH1, antioxidant 1 copper chaperone

ATOX1 is a copper metallochaperone protein that is encoded by the ATOX1 gene in humans. In mammals, ATOX1 plays a key role in copper homeostasis as it delivers copper from the cytosol to transporters ATP7A and ATP7B. Homologous proteins are found in a wide variety of eukaryotes, including Saccharomyces cerevisiae as ATX1, and all contain a conserved metal binding domain.

Gene data

ATOX1
Name
antioxidant 1 copper chaperone
Type
protein-coding
Aliases
ATX1, HAH1

This gene encodes a copper chaperone that plays a role in copper homeostasis by binding and transporting cytosolic copper to ATPase proteins in the trans-Golgi network for later incorporation to the ceruloplasmin. This protein also functions as an antioxidant against superoxide and hydrogen peroxide, and therefore, may play a significant role in cancer carcinogenesis. Because of its cytogenetic location, this gene represents a candidate gene for 5q-syndrome. [provided by RefSeq, Jul 2008].

via MyGene.info

Gene · Ensembl

antioxidant 1 copper chaperone

Symbol
ATOX1
Biotype
Protein coding
Organism
Homo sapiens
Location
5:151,728,919-151,772,532
Strand
Reverse (−)
Assembly
GRCh38
View on Ensembl →

via Ensembl · EMBL-EBI

Wikidata facts

Image
Protein ATOX1 PDB 1fe0.png
Show 5 more facts
HomoloGene ID
2984
genomic end
151152093
genomic start
151121877
cytogenetic location
5q33.1
Sources (4)

via Wikidata · CC0

~4 min read

Article

7 sections
Contents
  • Function
  • Structure & metal coordination
  • Metal transfer
  • Clinical significance
  • References
  • External links
  • Further reading

ATOX1 is a copper metallochaperone protein that is encoded by the ATOX1 gene in humans. In mammals, ATOX1 plays a key role in copper homeostasis as it delivers copper from the cytosol to transporters ATP7A and ATP7B. Homologous proteins are found in a wide variety of eukaryotes, including Saccharomyces cerevisiae as ATX1, and all contain a conserved metal binding domain.

== Function ==

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